Products and Kits
NameAssociated DiseaseGene (Mutation)Mutations / SampleTests / KitCatalog Number

PRONTO®

CF Euro I

Cystic Fibrosis

CFTR (F508del, G542X, W1282X, N1303K, 1717-1G>A, R1162X)

624F9946

PRONTO®

DNA Extraction kit (from human whole blood)
48 samplesF9925

PRONTO®

5FU
5-Fluorouracil sensitivityDPYD (IVS14+1G>A)1144F9984

PRONTO®

Gaucher

Gaucher

GBA (84GG, IVS2+1G>A, N370S [1226A>G], D409H [1342G>C], L444P [1448T>C], V394L [1297G>T])

624F9900

PRONTO®

Gaucher Screen

Gaucher

GBA (84GG, IVS2+1G>A, N370S [1226A>G], R496H [1604G>A], L444P [1448T>C], V394L [1297G>T])

624F9900-1

PRONTO®

ML4

Mucolipidosis IV

MCOLN1 (Del[ex1-7], IVS3-2A>G)

248F9960

PRONTO®

Niemann Pick

Niemann Pick Type A,
Type B

SMPD1 (L302P, fsP330, R496L, R608del)

436F9961

PRONTO®

FD

Familial Dysautonomia
(Riley Day Syndrome)

IKBKAP (2507+6T>C)

196F9948

PRONTO®

FD Screen

Familial Dysautonomia
(Riley Day Syndrome)

IKBKAP (2507+6T>C, R696P)

248F9963

PRONTO®

GSD

Glycogen Storage Disease Type 1a

G6PC (R83C)

1144F9967/2

PRONTO®

Joubert

Joubert Syndrome 2

TMEM216 c.35G>T (p.12R>L)

196F9987

PRONTO®

MNUG (MN format)

1. Maple Syrup Urine Disease 1b
2. Nemaline Myopathy 2

BCKDHB (R183P)

272F9975/1

PRONTO®

Tay-Sachs Ash

Tay-Sachs

HEXA (1278insTATC, G269S [805G>A], IVS12+1G>C)

348F9958

PRONTO®

Tay-Sachs Screen

Tay-Sachs

HEXA (1278insTATC,G269S, IVS12+1G>C, R170Q, IVS5-2A>G, F304del)

624F9981

PRONTO®

Usher

Usher Syndrome

PCDH15 (R245X)

1144F9967/1

PRONTO®

ProntoPlex™ AAT

Alpha-1 Antitrypsin Deficiency

SERPINA1 [AAT] (PiZ and PiS)

296F9965

PRONTO®

FMF Screen™

Familial Mediterranean Fever

MEFV (M680I, M694V, M694I, V726A, E148Q)

524F9904

PRONTO®

Hemochromatosis

Hereditary Hemochromatosis

HFE (C282Y, H63D, S65C)

332F9949

PRONTO®

ThromboRisk™

Predisposition to Thrombosis

F5 / Factor V (1691G>A) F2 / Factor II (20210G>A) MTHFR (677C>T)

332F9923

PRONTO®

Factor V

Predisposition to Thrombosis

F5 / Factor V (1691G>A)

196F9905

PRONTO®

Prothrombin

Predisposition to Thrombosis

F2 / Factor II (20210G>A)

196F9909

PRONTO®

MTHFR

Predisposition to Thrombosis

MTHFR (677C>T)

196F9910

PRONTO®

WarfaRisk™

Warfarin dosage

CYP2C9 (*2 [430C>T], *3 [1075A>C]) VKORC1(-1639G>A)

348F9979

PRONTO®

WarfaRisk+™

Warfarin dosage

CYP2C9 (*2 [430C>T], *3 [1075A>C]) VKORC1 (-1639G>A, 5417G>T)

436F9980

PRONTO®

ProntoTaq™ - HotStart Taq polymerase

50 µL
(5 units/µL)

F9101

PRONTO®

Connexin

Deafness

GJB2 connexin 26 (35delG, 167delT) GJB6 connexin 30 (del[GJB6-D13S1830])

348F9954

PRONTO®

2 GeneScreen

1.Mucolipidosis IV
2.Niemann Pick Type A, Type B

MCOLN1 (Del[ex 1-7],IVS3-2A>G)
SMPD1 (L302P, fsP330, R496L, R608del)

624F9954

PRONTO®

4 GeneScreen

1. Canavan
2. Bloom Syndrome
3. Fanconi Anemia C
4. Familial Dysautonomia

ASPA (693C>A, 854A>C) BLM (2281del6ins7) FANCC (IVS4+4A>T) IKBKAP (2507+6T>C, R696P)

624F9953

PRONTO®

Canavan

Canavan

ASPA (693C>A, 854A>C)

248F9906

PRONTO®

Bloom/Fanconi

1. Bloom Syndrome
2. Fanconi Anemia C

BLM (2281del6ins7) FANCC (IVS4+4A>T)

248F9931

PRONTO®

Ataxia/Fanconi A

1. Ataxia Telangiectasia
2. Fanconi Anemia A

ATM (103C>T) FANCA (2127-2173insG, 4275delT)

348F9982

PRONTO®

CF Basic

Cystic Fibrosis

CFTR (F508del, G542X, W1282X, N1303K, 3849+10KbC>T)

524F9901

PRONTO®

CF Basic+

Cystic Fibrosis

CFTR (F508del, G542X, W1282X, N1303K, 3849+10KbC>T, D1152H)

624F9943

PRONTO®

CF Open (choose 1-8 desired mutations)

Cystic Fibrosis

CFTR (S549R, G85E, D1152H, W1089X, 1717-1G>A, 405+1G>A, Q359K/T360K, 4010delTATT)

896F9920

PRONTO®

CFTR 5T

Cystic Fibrosis
CBAVD - congenital
bilateral absence
of the vas deferens

CFTR (5T/7T/9T)

148F9945

PRONTO®

AAT

Alpha-1 Antitrypsin Deficiency

SERPINA1 [AAT] (PiZ)

1144F9971

PRONTO®

ApoE

Predisposition to Hypercholesterolemia, Cardiovascular Disease

APOE (ε2, ε3, ε4)

248F9903

PRONTO®

APC

Predisposition to Colorectal Cancer

APC (3920T>A)

196F9907

PRONTO®

BRCA

Predisposition to Breast and Ovarian Cancer

BRCA1 (185delAG, 5382insC) BRCA2 (6174delT)

348F9911

PRONTO®

ClopidoRisk™

Clopidogrel metabolism

CYP2C19 (*2,*3,*4,*5) ABCB1 (3435C>T)

524F9985